[Neonatal segmental cystic nephroma. A case report]

Abstract

Multicystic segmental renal dysplasia is rare in early childhood. We report a case with prenatally recognized renal malformation. Prenatally a cystic renal malformation was detected sonographically; postnatally further evaluation was performed by Doppler sonography, contrast enhanced CT and voiding cysto-urethrography leading to the diagnosis of a multicystic segmental nephroma. Due to increasing size in spite of therapeutic and diagnostic sonographic guided punctures and the atypic manifestation the baby underwent heminephrectomy. The final histological diagnosis confirmed preoperativ findings.

Conclusion: Prenatally recognised cystiform renal malformations should be reevaluated postpartally by ultrasound and--as doubtful findings are found--further imaging might be necessary for follow up and for the decision on conservative or operative treatment.