Hernia uterus inguinale in a 46,XX female. A case report

Abstract

Background: Hernia uterus inguinale, a rare congenital anomaly, is usually found in hermophrodites.

Case: A case of lateral fusion defect associated with müllerian duct development in a young woman with primary amenorrhea and normal karyotype occurred. In our patient, bilateral müllerian duct systems were rudimentary and failed to fuse in the midline. The left horn of the uterus and ipsilateral ovary lay in the left inguinal canal. The right horn of the uterus, along with the tube and ovary, was intraabdominal.

Conclusion: In the operative management of this rare anomaly, care must be taken to preserve and reposition the ovary in the abdominal cavity.