Pulmonary problems in Duchenne muscular dystrophy. Diagnosis, prophylaxis, and treatment

Abstract

A number of pulmonary problems may complicate muscular dystrophy. Respiratory function, however, can be increased by instruction in diaphragmatic breathing. When patients effectively use their diaphragms during respiration, less muscular work is required for adequate ventilation. Additionally, assistive techniques such as postural drainage, chest percussion and vibration, and IPPB contribute to an ongoing program of respiratory care. Ten children with Duchenne muscular dystrophy underwent pulmonary function studies before, during, and after a three-month period of such respiratory therapy. Comparison of respiratory function before and after treatment indicates that such treatment is useful in increasing pulmonary function. The major goal of pulmonary care in the treatment of the patient with muscular dystrophy is the maintenance of respiratory homeostasis through beathing exercises and training in the use of various breathing aids, thus enabling the patient to lead as active and comfortable a life as possible within the limits imposed by his evolving respiratory problem.