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Case Reports
. 2000 Sep;21(8):1483-5.

Abnormal white matter signal in ataxia telangiectasia

Affiliations
Case Reports

Abnormal white matter signal in ataxia telangiectasia

J J Ciemins et al. AJNR Am J Neuroradiol. 2000 Sep.

Abstract

We report herein the MR finding of multiple, small, hypointense white matter foci on T1- and T2-weighted images obtained from a patient with ataxia telangiectasia. To our knowledge, this finding has not been previously reported in association with a patient with this disease entity.

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Figures

<sc>fig</sc> 1.
fig 1.
Images from the case of a 31-year-old woman with a 20-year history of ataxia telangiectasia who was admitted to the hospital after complaining of dizziness, headaches, and mood changes. A, Spin-echo sagittal T1-weighted (600/20/1 [TR/TE/excitations]) MR image shows cerebellar atrophy. B, Spin-echo axial T1-weighted (600/20/1) MR image shows multiple hypointense foci in the white matter bilaterally. C, Spin-echo axial T2-weighted (2900/80/1) MR image shows multiple hypointense foci in the white matter bilaterally.

References

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