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Case Reports
. 2000;27(3):309-11.

Gadolinium-enhanced magnetic resonance angiography in scimitar syndrome: diagnosis and postoperative evaluation

R C Gilkeson  1 , J H Lee, P B Sachs, M Clampitt
Affiliations
Case Reports

Gadolinium-enhanced magnetic resonance angiography in scimitar syndrome: diagnosis and postoperative evaluation

R C Gilkeson et al. Tex Heart Inst J. 2000.

Abstract

We report the 1st magnetic resonance demonstration of both an anomalous pulmonary venous drainage and systemic arterial supply in a patient with scimitar syndrome. With its superior imaging capabilities, gadolinium-enhanced magnetic resonance angiography provides a powerful diagnostic tool for this complex congenital lesion and offers the possibility of surgical repair and follow-up without conventional cardiac catheterization.

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Figures

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Fig. 1 Gadolinium-enhanced magnetic resonance angiography shows a large scimitar vein that drains most of the right lung into the intrahepatic inferior vena cava (solid arrows). Note the 2 abdominal aortic branches, which supply the right lower lobe and diaphragm (open arrows).
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Fig. 2 Delayed image from a pulmonary arteriogram confirms the presence of the scimitar vein draining into the intrahepatic inferior vena cava (long arrow). Note early filling of the right atrium (short arrow).
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Fig. 3 Abdominal aortography confirms the presence of a systemic artery that supplies the right basilar segments (arrows).
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Fig. 4 Postoperative gadolinium-enhanced magnetic resonance angiography shows the redirected scimitar vein draining into the left atrium (solid arrows). Note ligation of the systemic arterial supply (open arrows).
See this image and copyright information in PMC

References

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