Basal forebrain malformation with hyperhidrosis and hypothermia: variant of Shapiro's syndrome
- PMID: 11160966
- DOI: 10.1212/wnl.56.2.254
Basal forebrain malformation with hyperhidrosis and hypothermia: variant of Shapiro's syndrome
Abstract
A 62-year-old woman presented with episodic sweating and shivering with reduced core temperature. Brain MRI demonstrated a basal forebrain malformation. Physiologic testing included EEG, SPECT, heat challenge, and autonomic testing. Glycopyrrolate aborted spells and raised core temperature. Hypothalamic dysregulation is likely the primary pathophysiology in the setting of other forebrain anomalies. These findings expand the structural abnormalities and treatment options within the temperature dysregulating conditions of Shapiro's syndrome and "diencephalic epilepsy."
Comment in
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Basal forebrain malformation with hyperhidrosis and hypothermia: variant of Shapiro's syndrome.Neurology. 2002 Feb 12;58(3):508-9. doi: 10.1212/wnl.58.3.508. Neurology. 2002. PMID: 11839874 No abstract available.
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