Spontaneous regression of cerebral arteriovenous malformation in hereditary hemorrhagic telangiectasia

Abstract

Cerebral arteriovenous malformations (AVMs) are associated with hereditary hemorrhagic telangiectasia (HHT). I report a case of a patient with HHT with four cerebral AVMs in whom one AVM spontaneously regressed during a 5-year period. The spontaneous regression of this AVM in this patient with HHT supports the theory that AVMs associated with this syndrome have a different natural history than that of typical sporadic AVMs.

Fig 1.

Lateral projection angiograms. A, An AVM is fed by the posterior inferior cerebellar artery. B, Five years later, spontaneous resolution of the AVM has occurred.