Systemic capillary leak syndrome
- PMID: 12487166
- DOI: 10.2169/internalmedicine.41.953
Systemic capillary leak syndrome
Abstract
Systemic capillary leak syndrome (SCLS) is characterized by recurrent hypovolemic shock attributable to increased systemic capillary leakage. A 46-year-old man was admitted to our hospital because of recurrent episodes of generalized edema with hypovolemic shock. Blood laboratory data revealed severe hypoproteinemia with a small monoclonal IgG-kappa protein. These findings suggested strongly the diagnosis of SCLS. A regimen with steroid pulse therapy was tried; however, intravascular overloading accompanied by the recruitment of the initially extravasated fluids resulted in acute pulmonary edema. Intensive care and careful monitoring of fluid volume are required in SCLS.
Comment in
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Systemic capillary leak syndrome.Intern Med. 2002 Nov;41(11):909-10. doi: 10.2169/internalmedicine.41.909. Intern Med. 2002. PMID: 12487153 No abstract available.
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