Fatal interstitial pulmonary fibrosis in anti-Jo-1-negative amyopathic dermatomyositis
- PMID: 12894081
- DOI: 10.1067/s0190-9622(03)01482-8
Fatal interstitial pulmonary fibrosis in anti-Jo-1-negative amyopathic dermatomyositis
Abstract
Amyopathic dermatomyositis (DM) describes a subpopulation with the cutaneous eruption of DM, but without muscle involvement. Interstitial pulmonary fibrosis is a recognized complication of DM, often correlated with antisynthetase enzymes, such as anti-Jo-1. We describe a case of fatal IPF in a patient with anti-Jo-1 antibody-negative amyopathic DM.
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