[Anterior lenticonus, suggesting Alport syndrome. Apropos of a first case in Zaire]

Abstract

Anterior lenticonus is a rare condition, in which there is a conical or spherical protrusion of the anterior surface into the anterior chamber. This is demonstrated by this case report, which has not been previously described in the Black African or Zairian ophthalmological literature. The patient was 28 years old and complained of gradual deterioration of vision over several years. The visual acuity was 20/200. The slit lamp biomicroscope showed an anterior lenticonus with microopacities of the lens. On fundus examination, a fundus albipunctatus-like appearance with midperipheral retinal flecks and macular hole were found. The presence of associated ocular abnormalities, deafness and hematuria, is suggestive of Alport's syndrome.