Case Reports
doi: 10.1136/hrt.68.9.323.
Fabry's disease with complete atrioventricular block: histological evidence of involvement of the conduction system
Affiliations
- PMID: 1389767
- PMCID: PMC1025080
- DOI: 10.1136/hrt.68.9.323
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Case Reports
Fabry's disease with complete atrioventricular block: histological evidence of involvement of the conduction system
Br Heart J.
1992 Sep.
Abstract
A 63 year old man with complete atrioventricular block was diagnosed as having Fabry's disease. A short PR interval is a common electrocardiographic finding in Fabry's disease, but complete atrioventricular block is a very rare complication. Necropsy indicated that lipid accumulation in the atrioventricular conduction system was the probable cause of this patient's atrioventricular block.
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