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Case Reports
. 1992 Sep;68(3):323-5.
doi: 10.1136/hrt.68.9.323.

Fabry's disease with complete atrioventricular block: histological evidence of involvement of the conduction system

Y Ikari  1 , K Kuwako, T Yamaguchi
Affiliations
Case Reports

Fabry's disease with complete atrioventricular block: histological evidence of involvement of the conduction system

Y Ikari et al. Br Heart J. 1992 Sep.

Abstract

A 63 year old man with complete atrioventricular block was diagnosed as having Fabry's disease. A short PR interval is a common electrocardiographic finding in Fabry's disease, but complete atrioventricular block is a very rare complication. Necropsy indicated that lipid accumulation in the atrioventricular conduction system was the probable cause of this patient's atrioventricular block.

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