Osteofibrous dysplasia: a review of the literature and presentation of an additional 3 cases

Abstract

Osteofibrous dysplasia is a rare fibro-osseous lesion of uncertain etiology that occurs exclusively in the pediatric population. Diagnosis and treatment are complicated by the fact that osteofibrous dysplasia can resemble monostotic fibrous dysplasia and adamantinoma of long bones grossly and microscopically and that it tends to recur if surgical intervention is performed before skeletal maturity is reached. We present 3 cases of this lesion seen at our institution and provide a review of all previous cases reported in the literature.