Polysplenia syndrome with various visceral anomalies in an adult: embryological and clinical considerations
- PMID: 1477462
- DOI: 10.2169/internalmedicine.31.1026
Polysplenia syndrome with various visceral anomalies in an adult: embryological and clinical considerations
Abstract
A 26-year-old female with polysplenia syndrome is reported. She had numerous visceral anomalies including polysplenia, a short pancreas, a preduodenal portal vein, malrotation of the bowel, azygos continuation of the inferior vena cava, bilateral hyparterial bronchi and symmetrical liver lobation. Embryological and clinical considerations of polysplenia syndrome are described.
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