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Case Reports
. 2004 Mar;25(3):498-500.

Lacrimal location of sinus histiocytosis (Rosai-Dorfman-Destombes disease)

Robin Azoulay  1 , Hervé Brisse, Paul Fréneaux, Solène Ferey, Gabriel Kalifa, Catherine Adamsbaum
Affiliations
Case Reports

Lacrimal location of sinus histiocytosis (Rosai-Dorfman-Destombes disease)

Robin Azoulay et al. AJNR Am J Neuroradiol. 2004 Mar.

Abstract

A 7-year-old West African male patient presented with recurrence of multiple cervical lymphadenopathy. Cervical node biopsy disclosed a sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman-Destombes disease). During follow-up, the patient developed a left orbital mass corresponding to an enlarged lacrimal gland shown by CT. The histologic features of the gland were consistent with the diagnosis, and with steroid treatment, the gland decreased in size. Although rare, the diagnosis of sinus histiocytosis with massive lymphadenopathy has to be considered in cases of lacrimal gland enlargement.

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Figures

F<sc>ig</sc> 1.
Fig 1.
Coronal view CT reconstruction. A, Presence of an extraconal mass corresponding to the enlarged lacrimal gland on the left side. B, Absence of destruction of bone.
See this image and copyright information in PMC

References

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