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Case Reports
. 2004 Aug;90(8):918-20.
doi: 10.1136/hrt.2003.024760.

Persistent pulmonary hypertension late after neonatal aortic valvotomy: a consequence of an expanded surgical cohort

M Burch  1 , L Kaufman, N Archer, I Sullivan
Affiliations
Case Reports

Persistent pulmonary hypertension late after neonatal aortic valvotomy: a consequence of an expanded surgical cohort

M Burch et al. Heart. 2004 Aug.

Abstract

Background: Survival of neonates with critical aortic stenosis has improved over the past decade. Models based on morphological characteristics have been designed to help determine whether early survival is more likely after biventricular repair (surgical or balloon aortic valvotomy) or after a single ventricle staged palliative surgical strategy. However, late follow up data are lacking.

Objective: To report follow up data on survivors of neonatal aortic valvotomy who had persistent pulmonary hypertension caused by restriction to left ventricular filling.

Results: Of four medium term survivors of neonatal valvotomy for critical aortic stenosis who had persistent pulmonary hypertension, one died aged 4 years and the other three have severe limitation of effort tolerance.

Conclusions: This previously unreported late complication of "successful" biventricular repair for neonatal critical aortic stenosis is an important consideration in determining the initial management.

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Figures

Figure 1
Figure 1
Light microscopy from operative myocardial biopsy in case 3 showing notable fibroelastic thickening of the left ventricular endocardium. (By courtesy of Dr A Ramsay.)
Figure 2
Figure 2
Fetal echocardiography in case 4: transverse thoracic view showing bright endocardial echoes. The spine is labelled for orientation. AO, aorta; LV, left ventricle; RV, right ventricle.
See this image and copyright information in PMC

References

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