Initial management of complex pediatric disorders: prunebelly syndrome, posterior urethral valves
- PMID: 15313050
- DOI: 10.1016/j.ucl.2004.04.010
Initial management of complex pediatric disorders: prunebelly syndrome, posterior urethral valves
Abstract
Prunebelly syndrome and posterior urethral valves are conditions of detrusor dysfunction associated with antenatal urethral obstruction. The resultant severe hydroureteronephrosis and renal dysplasia initiate a sequence potentially leading to renal failure. This article reviews clinical features and explores neonatal evaluation and treatment for both conditions. A comprehensive approach to initial management aimed at optimal renal preservation and bladder rehabilitation is proposed.
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