The first case of primary retroperitoneal mucinous cystadenoma in Korea: a case report

Abstract

Primary mucinous cystic cystadenomas of the retroperitoneum are very rarely encountered, and there have been only about 30 cases reported in the literature. The histogenesis of primary mucinous cystadenomas is unclear. Most authors suggested that it develops through mucinous metaplasia in a pre-existing mesothelium-lined cyst. Complete surgical excision is the only treatment and it is required for the final diagnosis and cure. We present here a case report of a 38-year-old Korean woman with primary retroperitoneal cystadenoma. It was a thin-walled, multilocular cyst with a dominant loculus that measured 10.0 x 7.5 x 5.5 cm3 in size, and to the best of our knowledge, this is the first such case to be reported in in Korea.

Figure 1.

Abdominal CT showed the retroperitoneal mass had displaced the right colon medially and this encapsulated cystic mass contained fluids.

Figure 2.

Multilocular cyst lined by a single layer of tall columnar cells. The stroma consisted of fibrocollagenous tissue with no pancreatic or ovarian components (H & E, ×40).

Figure 3.

The cells had clear cytoplasm and basely located small nuclei with no cytologic atypia (H & E, ×200).

Figure 4.

On immunohistochemical staining, the lining cells showed positive reactions to CAM 5.2 (×200).