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Case Reports
. 2005 May 11;101(1):147-50.
doi: 10.1016/j.ijcard.2004.01.027.

Kearns-Sayre syndrome associated with trifascicular block and QT prolongation

Pavlos Karanikis, Panagiotis Korantzopoulos, Evaggelos Kountouris, Vasiliki Dimitroula, Dimitrios Patsouras, Eugenia Pappa, Konstantinos Siogas
Case Reports

Kearns-Sayre syndrome associated with trifascicular block and QT prolongation

Pavlos Karanikis et al. Int J Cardiol. .

Abstract

Patients suffering from Kearns-Sayre syndrome (KSS) often develop conduction defects that may lead to syncope or sudden cardiac death. The association of conduction abnormalities with prolonged QT interval in these patients is very rare. We describe a patient with KSS and diabetes mellitus who suffered a torsades de pointes-induced syncopal attack, in the presence of trifascicular block and QT prolongation (QTc: 574 ms). The patient was successfully treated with permanent pacing. This case highlights that torsades de pointes represents a potential mechanism of syncope or sudden cardiac death in patients with KSS.

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