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Case Reports
. 1992 Mar;68(797):192-5.
doi: 10.1136/pgmj.68.797.192.

Adult metachromatic leukodystrophy with an unusual relapsing-remitting course

M Sadeh  1 , A Kuritzky, E Ben-David, Y Goldhammer
Affiliations
Case Reports

Adult metachromatic leukodystrophy with an unusual relapsing-remitting course

M Sadeh et al. Postgrad Med J. 1992 Mar.

Abstract

A 46 year old woman had a relapsing-remitting course of hemiparesis, disorientation, paraparesis and seizures, followed by progressive dementia, spasticity and ataxia. Computed tomography at onset showed a parietotemporal hypodense area with diffuse mottled enhancement obliterating the lateral ventricle. Subsequent scans demonstrated symmetric periventricular non-enhancing hypodensities, progressive ventricular enlargement and atrophy. Adult metachromatic leukodystrophy was diagnosed on the basis of low leukocyte arylsulphatase A level and metachromatic material accumulation at neural nerve biopsy.

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