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Review
. 2005 Aug;29(4):210-3.
doi: 10.1007/s00264-005-0641-y. Epub 2005 May 18.

Desmoid tumours of the extremities and trunk: a review of the literature

Emilios E Pakos  1 , Pericles G Tsekeris, Ann C Goussia
Affiliations
Review

Desmoid tumours of the extremities and trunk: a review of the literature

Emilios E Pakos et al. Int Orthop. 2005 Aug.

Abstract
in English, French

Desmoid tumours are rare neoplasms that display local aggressiveness but no propensity to metastasise. They are mainly localized in the abdominal wall, the bowel, and the mesentery or in extra-abdominal sites such as the trunk and the extremities. Surgical resection is the main treatment modality in extremities and trunk, with the optional combination of radiotherapy and/or chemotherapy. However, these tumours have a high propensity for recurrent growth.

Les tumeurs desmoides sont des néoplasmes rares qui ont un caractère agressif local, mais aucune propension à métastaser. Elles sont principalement localisés dans la paroi abdominale, l’intestin et le mésentère et dans des sites extra-abdominaux tels que le tronc et les extrémités. La résection chirurgicale est la principale modalité du traitement pour les extrémités et le tronc avec la combinaison facultative de radiothérapie et/ou chimiothérapie. Cependant, ils ont une haute tendance à la récidive.

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