Review
Recurrent Lhermitte-Duclos disease: report of two cases and association with Cowden's disease
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- PMID: 1595461
- PMCID: PMC8331774
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Review
Recurrent Lhermitte-Duclos disease: report of two cases and association with Cowden's disease
AJNR Am J Neuroradiol.
1992 Jan-Feb.
Abstract
Two cases of Lhermitte-Duclos disease (LDD), one associated with Cowden's disease, are reported. Both demonstrated recurrence long after initial surgical resection. There is a propensity for occurrence in the left cerebellar hemisphere. On MR there is hypointensity on T1-weighted images and moderately high signal on T2-weighted images, with parallel linear striations on the surface of the lesion felt to represent dysplastic cerebellar folia. LDD is felt to be a low-grade neoplasm and potential component of Cowden's phakomatosis.
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