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Review
. 2005 Jul;11(7):834-838.
doi: 10.1002/lt.20463.

Liver transplantation for cardiac failure in patients with hereditary hemorrhagic telangiectasia

Thierry Thevenot  1 , Claire Vanlemmens  1 , Vincent Di Martino  1 , Marie-Claude Becker  1 , Pierre-Olivier Denue  2 , Bernadette Kantelip  3 , Solange Bresson-Hadni  1 , Bruno Heyd  2 , Georges Mantion  2 , Jean-Philippe Miguet  1
Affiliations
Free article
Review

Liver transplantation for cardiac failure in patients with hereditary hemorrhagic telangiectasia

Thierry Thevenot et al. Liver Transpl. 2005 Jul.
Free article

Abstract

Liver involvement in hereditary hemorrhagic telangiectasia may lead to high-output cardiac failure. Few data have been reported on orthotopic liver transplantation (OLT) for these patients. In this paper, we describe two patients treated by OLT as a salvage procedure for cardiac failure, and we review literature on this subject. Our two patients resumed normal cardiac function after OLT. This procedure appears to be a promising therapy with good long-term results despite dissection difficulties encountered due to the collateral arterial network reorganization.

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References

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