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Case Reports
. 2006 Apr;15(4):433-9.
doi: 10.1007/s00586-005-0980-9. Epub 2005 Sep 20.

Infantile scoliosis in Beals syndrome: the use of a non-fusion technique for surgical correction

Anthony Gwynne Martin  1 , Pedro R Foguet, David S Marks, A G Thompson, A H Child
Affiliations
Case Reports

Infantile scoliosis in Beals syndrome: the use of a non-fusion technique for surgical correction

Anthony Gwynne Martin et al. Eur Spine J. 2006 Apr.

Abstract

Beals syndrome (congenital contractural arachnodactyl) is a genetic disorder of the connective tissue phenotypically related to Marfan syndrome. It is characterised by dolichostenomelia, arachnodactyly, multiple joint contractures, crumpled ears, hypoplastic muscles and scoliosis. The latter, the most important clinical feature of this rare condition, presents in the infantile and juvenile age group and has a tendency to rapid progression. Bracing often fails to control the scoliosis and surgery is the recommended treatment. We present our experience of two cases managed with the paediatric Isola instrumentation and a non-fusion technique.

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Figures

Fig. 1
Fig. 1
a, b Preoperative radiographs of case number 1
Fig. 2
Fig. 2
a, b Postoperative radiographs of case number 1 immediately after implantation of paediatric Isola
Fig. 3
Fig. 3
Preoperative radiograph of case number 2
Fig. 4
Fig. 4
a, b Initial post-operative radiographs case 2
Fig. 5
Fig. 5
a, b Final radiographs of case number 2
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