Life-threatening gross hematuria due to genitourinary manifestation of Klippel-Trenaunay syndrome
- PMID: 16502069
- DOI: 10.1007/s11255-005-3154-0
Life-threatening gross hematuria due to genitourinary manifestation of Klippel-Trenaunay syndrome
Abstract
The Klippel-Trenaunay Syndrome (KTS) is defined as a triad of cutaneous capillary malformations, venous varicosities, bone and soft tissue hemi-hypertrophy. The urinary tract is involved in up to 10%. We report the clinical presentation and surgical management of a 9-year-old boy with extensive lympho-venous malformations of the bladder which led to massive recurrent gross hematuria.
Similar articles
-
Recurrent hematuria involving urinary system with Klippel-Trenaunay syndrome: A case report.Medicine (Baltimore). 2024 Feb 16;103(7):e36923. doi: 10.1097/MD.0000000000036923. Medicine (Baltimore). 2024. PMID: 38363945 Free PMC article.
-
Lower gastrointestinal bleeding, hematuria and splenic hemangiomas in Klippel-Trenaunay syndrome: a case report and literature review.Turk J Gastroenterol. 2009 Mar;20(1):62-6. Turk J Gastroenterol. 2009. PMID: 19330738 Review.
-
Massive hematuria in adults with Klippel-Trenaunay syndrome associated with vascular malformation of the bladder.Urol Int. 2000;64(4):226-8. doi: 10.1159/000030537. Urol Int. 2000. PMID: 10895091
-
Klippel-Trenaunay syndrome: incidence and treatment of genitourinary sequelae.J Urol. 2007 Apr;177(4):1244-9. doi: 10.1016/j.juro.2006.11.099. J Urol. 2007. PMID: 17382698 Review.
-
The Klippel-Trenaunay syndrome: a rare cause of hematuria requiring nephrectomy.J Urol. 1994 Feb;151(2):404-5. doi: 10.1016/s0022-5347(17)34962-5. J Urol. 1994. PMID: 8283536
Cited by
-
Sclerotherapy treatment of a large venous malformation invading the bladder wall related to Klippel-Trenaunay syndrome.BMJ Case Rep. 2020 Dec 21;13(12):e229823. doi: 10.1136/bcr-2019-229823. BMJ Case Rep. 2020. PMID: 33370935 Free PMC article.
-
A rare case of a 5-year-old girl with Klippel-Trénaunay syndrome and a bleeding focal vulvar hemangioma in Uganda.Clin Case Rep. 2024 Oct 21;12(10):e9501. doi: 10.1002/ccr3.9501. eCollection 2024 Oct. Clin Case Rep. 2024. PMID: 39440347 Free PMC article.
-
Klippel-Trenaunay Syndrome, Segmental/Focal Overgrowth Malformations: A Review.Children (Basel). 2023 Aug 21;10(8):1421. doi: 10.3390/children10081421. Children (Basel). 2023. PMID: 37628420 Free PMC article. Review.
-
Recurrent hematuria involving urinary system with Klippel-Trenaunay syndrome: A case report.Medicine (Baltimore). 2024 Feb 16;103(7):e36923. doi: 10.1097/MD.0000000000036923. Medicine (Baltimore). 2024. PMID: 38363945 Free PMC article.
-
Case Report: Life-Threatening Post-operative Hemorrhage in Klippel-Trenaunay Syndrome Associated With Hypofibrinogenemia.Front Med (Lausanne). 2021 Aug 9;8:669793. doi: 10.3389/fmed.2021.669793. eCollection 2021. Front Med (Lausanne). 2021. PMID: 34434940 Free PMC article.
References
Publication types
MeSH terms
LinkOut - more resources
Full Text Sources
Medical