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Case Reports
. 2006 Oct 15;47(5):636-8.
doi: 10.1002/pbc.20787.

Primary malignant peripheral nerve sheath tumor of the lung in a young child without neurofibromatosis type 1

Samar A Muwakkit  1 , Carlos Rodriguez-Galindo, Ahmad I El Samra, Ruby Khoury, Samir R Akel, Salman Mroueh, Bassem Razzouk, Miguel R Abboud
Affiliations
Case Reports

Primary malignant peripheral nerve sheath tumor of the lung in a young child without neurofibromatosis type 1

Samar A Muwakkit et al. Pediatr Blood Cancer. .

Abstract

Malignant peripheral nerve sheath tumors (MPNST) are uncommon in children and almost half of the cases occur in patients with neurofibromatosis 1 (NF1). We report a child with a primary MPNST of the lung without NF1. MPNST of the lung has similar clinical and radiologic characteristics as pleuropulmonary blastoma. We suggest to include MPNST of the lung in the differential diagnosis of intrapulmonary masses in children.

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