Scleromyxedema: An experience using treatment with systemic corticosteroid and review of the published work
- PMID: 16620228
- DOI: 10.1111/j.1346-8138.2006.00047.x
Scleromyxedema: An experience using treatment with systemic corticosteroid and review of the published work
Abstract
Scleromyxedema, a rare cutaneous mucinosis of unknown cause, is a variant of generalized papular mucinosis that is also known as generalized lichen myxedematosus. It is characterized clinically by generalized papular or scleroderma-like eruptions. Histopathological examination reveals mucin deposition and a proliferation of fibroblasts in the upper dermis. We describe the case of a man with scleromyxedema treated with systemic corticosteroids whose skin lesions improved gradually within 4 weeks.
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