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. 2006 Aug 7:4:48.
doi: 10.1186/1477-7819-4-48.

Clear cell sarcoma of the scapula. A case report and review of the literature

Constantinos J Kazakos  1 , Vasilios G Galanis, Alexandra Giatromanolaki, Dennis-Alexander J Verettas, Efthimios Sivridis
Affiliations

Clear cell sarcoma of the scapula. A case report and review of the literature

Constantinos J Kazakos et al. World J Surg Oncol. .

Abstract

Background: Clear cell sarcoma of tendons and aponeuroses (CCSTA) appears usually in the extremities and rarely in the trunk.

Case presentation: We present an unusual case of CCSTA overlying the scapular region and with secondary osseous extension in the lower scapula. The patient underwent a wide local excision with removal of the tumor and the lower two thirds of the scapula. He had no local recurrences but he developed lung metastases after 5 months in spite of postoperative chemotherapy. He finally died ten months later.

Conclusion: The patients with CCSTA have a variable unpredictable course. Despite treatment the overall prognosis is poor.

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Figures

Figure 1
Figure 1
Axial CT scan revealed a soft tissue mass localized in the lower scapular region with intralesional calcifications and a secondary osseous invasion of the lower scapula.
Figure 2
Figure 2
MRI image established the tumor measuring 45 × 45 mm.
Figure 3
Figure 3
Saggital MRI image through the scapular region showed the soft tissue tumor.
Figure 4
Figure 4
Clear cell sarcoma tissue section: compact nests and fascicles with large rounded and spindle-shaped cells separated by connective tissue septa. Mitoses are numerous. The cells had large amounts of clear cytoplasm (H&E ×200).
Figure 5
Figure 5
Immunohistochemical staining for S-100 showing cytoplasmic positivity. Magnification ×200.
See this image and copyright information in PMC

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