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Review
. 2006 Oct;77(10):1108-15.
doi: 10.1136/jnnp.2005.078881.

Respiratory involvement in inherited primary muscle conditions

N Shahrizaila  1 , W J M Kinnear, A J Wills
Affiliations
Review

Respiratory involvement in inherited primary muscle conditions

N Shahrizaila et al. J Neurol Neurosurg Psychiatry. 2006 Oct.

Abstract

Patients with inherited muscle disorders can develop respiratory muscle weakness leading to ventilatory failure. Predicting the extent of respiratory involvement in the different types of inherited muscle disorders is important, as it allows clinicians to impart prognostic information and offers an opportunity for early interventional management strategies. The approach to respiratory assessment in patients with muscle disorders, the current knowledge of respiratory impairment in different muscle disorders and advice on the management of respiratory complications are summarised.

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Conflict of interest statement

Competing interests: None declared.

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