Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Review
. 2006 Oct;77(10):1108-15.
doi: 10.1136/jnnp.2005.078881.

Respiratory involvement in inherited primary muscle conditions

N Shahrizaila  1 , W J M Kinnear, A J Wills
Affiliations
Review

Respiratory involvement in inherited primary muscle conditions

N Shahrizaila et al. J Neurol Neurosurg Psychiatry. 2006 Oct.

Abstract

Patients with inherited muscle disorders can develop respiratory muscle weakness leading to ventilatory failure. Predicting the extent of respiratory involvement in the different types of inherited muscle disorders is important, as it allows clinicians to impart prognostic information and offers an opportunity for early interventional management strategies. The approach to respiratory assessment in patients with muscle disorders, the current knowledge of respiratory impairment in different muscle disorders and advice on the management of respiratory complications are summarised.

PubMed Disclaimer

Conflict of interest statement

Competing interests: None declared.

References

    1. Gibson G J, Pride N B, Davis J N.et al Pulmonary mechanics in patients with respiratory muscle weakness. Am Rev Respir Dis 1977115389–395. - PubMed
    1. Davis J, Goldman M, Loh L.et al Diaphragm function and alveolar hypoventilation. Q J Med 19764587–100. - PubMed
    1. Griggs R C, Donohoe K M, Utell M J.et al Evaluation of pulmonary function in neuromuscular disease. Arch Neurol 1981389–12. - PubMed
    1. Ward N S, Hill N S. Pulmonary function testing in neuromuscular disease. Clin Chest Med 200122769–781. - PubMed
    1. ATS/ERS Statement on respiratory muscle testing. Am J Respir Crit Care Med 2002166518–624. - PubMed

MeSH terms