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Case Reports
. 2007 Mar;28(3):593-5.

Atypical teratoid/rhabdoid tumor of the spine

K K Moeller  1 , S Coventry, S Jernigan, T M Moriarty
Affiliations
Case Reports

Atypical teratoid/rhabdoid tumor of the spine

K K Moeller et al. AJNR Am J Neuroradiol. 2007 Mar.

Abstract

Atypical teratoid/rhabdoid tumor (AT/RT) is a highly malignant central nervous system neoplasm usually seen in young children and infants. Prognosis for AT/RT is poor, with most patients dying within 1 year of presentation. AT/RT most commonly occurs intracranially. Location in the spine, though previously reported, is rare, and imaging findings have not been emphasized in the past. We present a case of AT/RT occurring in the thoracolumbar spine of a child and review available clinical and imaging findings in previously reported cases of spinal AT/RT.

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Figures

Fig 1.
Fig 1.
A, Sagittal T1-weighted image demonstrates a mass filling the spinal canal from T11 through L2. The lesion is hypointense to cord. Hyperintense signal intensity filling the distal thecal sac demonstrated no enhancement on postcontrast images, consistent with hemorrhage or proteinaceous debris. B, On the sagittal T2-weighted image, the mass is isointense to cord with focal areas that are hypointense. The nerve roots are clumped distally, and there is edema in the cord rostrally. C, Sagittal postcontrast T1-weighted image shows diffuse enhancement of the mass. There is no additional enhancement in the distal thecal sac.
Fig 2.
Fig 2.
Rare cells with rhabdoid features (arrow), eccentric nuclei, and eosinophilic cytoplasmic hyaline inclusions (hematoxylin-eosin, ×600).
See this image and copyright information in PMC

References

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