Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2007 Jul-Aug;30(4):782-5.
doi: 10.1007/s00270-007-9009-6.

Pulmonary arterial stent implantation in an adult with Williams syndrome

Herre J Reesink  1 , Onno D F Henneman, Otto M van Delden, Jules D Biervliet, Jaap J Kloek, Jim A Reekers, Paul Bresser
Affiliations
Case Reports

Pulmonary arterial stent implantation in an adult with Williams syndrome

Herre J Reesink et al. Cardiovasc Intervent Radiol. 2007 Jul-Aug.

Abstract

We report a 38-year-old patient who presented with pulmonary hypertension and right ventricular dysfunction due to pulmonary artery stenoses as a manifestation of Williams syndrome, mimicking chronic thromboembolic pulmonary hypertension. The patient was treated with balloon angioplasty and stent implantation. Short-term follow-up showed a good clinical result with excellent patency of the stents but early restenosis of the segments in which only balloon angioplasty was performed. These stenoses were subsequently also treated successfully by stent implantation. Stent patency was observed 3 years after the first procedure.

PubMed Disclaimer

Figures

Fig. 1
Fig. 1
A Digital subtraction angiogram of the right pulmonary artery (oblique view) before treatment, demonstrating stenoses at the origin of the right superior lobe trunk, the middle lobe artery, and the lower lobe trunk (arrows). B Digital subtraction angiogram of the left pulmonary artery (oblique view) before treatment, demonstrating occlusion of the left upper lobe and multiple stenoses in the segmental branches of the lower lobe artery (arrows)
Fig. 2
Fig. 2
A Sagittal-oblique thick maximum intensity projection image of the multislice computed tomography angiogram (slice thickness 10 mm) before treatment, showing the stenotic right middle lobe artery (arrowhead). B Repeat computed tomography 6 months after stent placement in the right middle lobe artery in the same projection as in A
Fig. 3
Fig. 3
A, B Digital subtraction angiogram of the right A and left B pulmonary artery (oblique view) 3 years after the initial stenting procedure, showing excellent patency of the stents in the right upper, middle and lower lobe arteries and in the left lower lobe arteries (arrows)
See this image and copyright information in PMC

References

    1. {'text': '', 'ref_index': 1, 'ids': [{'type': 'DOI', 'value': '10.1056/NEJMra010902', 'is_inner': False, 'url': 'https://doi.org/10.1056/nejmra010902'}, {'type': 'PubMed', 'value': '11794196', 'is_inner': True, 'url': 'https://pubmed.ncbi.nlm.nih.gov/11794196/'}]}
    2. Fedullo PF, Auger WR, Kerr KM, et al. (2001) Chronic thromboembolic pulmonary hypertension. N Engl J Med 345:1465–1472 - PubMed
    1. {'text': '', 'ref_index': 1, 'ids': [{'type': 'DOI', 'value': '10.1056/NEJMoa032274', 'is_inner': False, 'url': 'https://doi.org/10.1056/nejmoa032274'}, {'type': 'PubMed', 'value': '15163775', 'is_inner': True, 'url': 'https://pubmed.ncbi.nlm.nih.gov/15163775/'}]}
    2. Pengo V, Lensing AW, Prins MH, et al. (2004) Incidence of chronic thromboembolic pulmonary hypertension after pulmonary embolism. N Engl J Med 350:2257–2264 - PubMed
    1. {'text': '', 'ref_index': 1, 'ids': [{'type': 'PubMed', 'value': '7599847', 'is_inner': True, 'url': 'https://pubmed.ncbi.nlm.nih.gov/7599847/'}]}
    2. Kerr KM, Auger WR, Fedullo PF, et al. (1995) Large vessel pulmonary arteritis mimicking chronic thromboembolic disease. Am J Respir Crit Care Med 152:367–373 - PubMed
    1. {'text': '', 'ref_index': 1, 'ids': [{'type': 'PubMed', 'value': '8641032', 'is_inner': True, 'url': 'https://pubmed.ncbi.nlm.nih.gov/8641032/'}]}
    2. Kreutzer J, Landzberg MJ, Preminger TJ, et al. (1996) Isolated peripheral pulmonary artery stenoses in the adult. Circulation 93:1417–1423 - PubMed
    1. {'text': '', 'ref_index': 1, 'ids': [{'type': 'DOI', 'value': '10.1016/S0003-4975(02)03414-8', 'is_inner': False, 'url': 'https://doi.org/10.1016/s0003-4975(02)03414-8'}, {'type': 'PubMed', 'value': '12078812', 'is_inner': True, 'url': 'https://pubmed.ncbi.nlm.nih.gov/12078812/'}]}
    2. Brister SJ, Wilson-Yang K, Lobo FV, et al. (2002) Pulmonary thromboendarterectomy in a patient with giant cell arteritis. Ann Thorac Surg 73:1977–1979 - PubMed

Publication types

MeSH terms