Review
doi: 10.1152/physiol.00044.2006.
Inherited renal acidoses
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- PMID: 17557941
- DOI: 10.1152/physiol.00044.2006
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Review
Inherited renal acidoses
Physiology (Bethesda).
2007 Jun.
Free article
Abstract
Inherited acidosis may result from a primary renal defect in acid-base handling, emphasizing the central role of the kidney in control of body pH; as a secondary phenomenon resulting from abnormal renal electrolyte handling; or from excess production of acid elsewhere in the body. Here, we review our current understanding of the inherited renal acidoses at a genetic and molecular level.
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