[Cystic fibrosis: how to use pulmonary function tests]

Abstract

Introduction: Neonatal screening for cystic fibrosis (CF) leads to early dedicated specialist care for all patients.

Background: Pulmonary function tests (PFT) are mandatory for routine monitoring of CF patients. The aim of this article is to review the current guidelines for PFTs in CF, particularly the type of test, the age and the clinical status of the patient.

Viewpoint: The regular use of spirometry is generally accepted. Many other tests are used but their clinical value in the routine follow-up of CF patients remains to be established.

Conclusion: Further efforts should be made to evaluate the value of PFTs in CF, particularly in very young children.