[Femoral osteosarcoma revealing onset of unifocal Paget's disease. Favourable course with 7-year follow-up]

Abstract

Sarcomatous degeneration is the most serious complication of Paget's disease, and few cases survive beyond 5 years. The authors report a new case, which occurred in a 62-year-old woman, in which calcifying periarthritis of the hip revealed the presence of a sarcoma developed in a context of a single bone case of Paget's disease affecting the upper extremity of the femur. Diagnosis was histological. The prognostic factors of Paget-related sarcomas are reviewed. The most important are the early timing of diagnosis and a site permitting radical surgical exeresis.