Case Reports
doi: 10.1111/j.1442-200x.1991.tb01884.x.
Successful dantrolene sodium treatment of a patient with myotonia congenita (Thomsen's disease)
Affiliations
- PMID: 1799124
- DOI: 10.1111/j.1442-200x.1991.tb01884.x
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Case Reports
Successful dantrolene sodium treatment of a patient with myotonia congenita (Thomsen's disease)
Acta Paediatr Jpn.
1991 Oct.
Abstract
A 3 year, 10 month old male with myotonia congenita (Thomsen's disease) was placed on dantrolene sodium, which successfully abolished the myotonic phenomenon. Dantrolene sodium might therefore be a useful medicine for patients with Thomsen's disease who do not respond to other medicines, such as carbamazepine (CBZ), with a decrease in the myotonic phenomenon.
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