Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Review
. 2007 Nov;30(6):880-7.
doi: 10.1007/s10545-007-0718-4. Epub 2007 Nov 25.

Nutritional management of patients with urea cycle disorders

R H Singh  1
Affiliations
Review

Nutritional management of patients with urea cycle disorders

R H Singh. J Inherit Metab Dis. 2007 Nov.

Abstract

The nutritional management of patients with urea cycle disorders (UCDs) involves restriction of dietary protein along with provision of adequate protein-free energy, essential amino acid supplements, and vitamins and minerals in combination with nitrogen-scavenging drugs. The present paper discusses nutrition therapy for a range of circumstances: during an acute hyperammonaemic episode and at hospital discharge; before, during, and after surgery; and for lifelong chronic management of UCDs.

PubMed Disclaimer

References

    1. Curr Opin Clin Nutr Metab Care. 2005 Jan;8(1):61-5 - PubMed
    1. J Pediatr. 2001 Jan;138(1 Suppl):S30-9 - PubMed
    1. Arch Dis Child. 2002 Jan;86(1):54-6 - PubMed
    1. Metab Brain Dis. 2005 Dec;20(4):303-18 - PubMed
    1. Crit Care Clin. 2005 Oct;21(4 Suppl):S27-35 - PubMed

Publication types

MeSH terms

LinkOut - more resources