A case of intrapericardial extralobar pulmonary sequestration--first case in Korea

Abstract

Extralobar pulmonary sequestration, known as accessory lung, is a rare congenital anomaly and intrapericardial lung sequestration is extremely rare. To the best of our knowledge, only four reported cases were intrapericardial. We report a case with intrapericardial extralobar pulmonary sequestration confirmed by operation and morphologic basis.

Fig. 1

Chest PA revealed well defined mediasthinal mass on the right paratracheal area.

Fig. 2

Chest CT scan revealed large multi-cystic mass lesion on the right paratracheal area which was attached to the lower pole of the right thyroid gland, displaced the superior vena cava anteriorly and extended to the level of the azygous vein.

Fig. 3

The mass is composed of several cystic lesions and yellow solid lesion resembling unexpanded lung tissue.

Fig. 4

The surface of the mass shows a feeding vessel (FV)

Fig. 5

The cyst wall shows a bronchial tissue which is composed of ciliated columnar epithelium, submucosal glands and cartilage (×100, H–E).

Fig. 6

The solid portion of the mass shows alveolar spaces filled with inflammatory cells (×200, H–E).