Review
doi: 10.1016/j.jbspin.2007.07.014.
Epub 2008 Feb 22.
Schnitzler syndrome
Affiliations
- PMID: 18378180
- DOI: 10.1016/j.jbspin.2007.07.014
Item in Clipboard
Review
Schnitzler syndrome
Joint Bone Spine.
2008 May.
Abstract
Schnitzler syndrome is characterized by monoclonal IgM gammopathy, urticaria, recurrent fever, evidence of inflammation, bone pain, and arthralgia, occasionally in combination with lymphadenopathy and/or hepatosplenomegaly. Only about 80 cases have been reported to date. Development of a hematological malignancy is the main complication. Recent reports of remissions induced by IL-1 receptor antagonist therapy shed new light on the pathophysiology of the disease.
Similar articles
-
Schnitzler Syndrome Without a Monoclonal Gammopathy: A Case Report.J Cutan Med Surg. 2016 Nov;20(6):575-578. doi: 10.1177/1203475416657999. Epub 2016 Jun 29. J Cutan Med Surg. 2016. PMID: 27358310
-
Chronic urticaria with monoclonal IgG gammopathy: a clinical variant of Schnitzler syndrome?Ann Allergy Asthma Immunol. 2012 Aug;109(2):147-8. doi: 10.1016/j.anai.2012.06.001. Ann Allergy Asthma Immunol. 2012. PMID: 22840258 No abstract available.
-
[Schnitzler syndrome].Hautarzt. 2018 Sep;69(9):761-772. doi: 10.1007/s00105-018-4250-2. Hautarzt. 2018. PMID: 30167710 German.
-
[Schnitzler syndrome: a rare cause of systemic urticaria].Rev Med Interne. 2000 Mar;21(3):285-9. doi: 10.1016/s0248-8663(00)80049-1. Rev Med Interne. 2000. PMID: 10763191 Review. French.
-
The Schnitzler syndrome: chronic urticaria and monoclonal gammopathy--an autoinflammatory syndrome?J Dtsch Dermatol Ges. 2008 Aug;6(8):626-31. doi: 10.1111/j.1610-0387.2008.06627.x. Epub 2008 Mar 14. J Dtsch Dermatol Ges. 2008. PMID: 18371052 Review. English, German.
Cited by
-
Schnitzler syndrome with cold-induced urticaria.J Dermatol Case Rep. 2010 Dec 31;4(4):50-3. doi: 10.3315/jdcr.2010.1060. J Dermatol Case Rep. 2010. PMID: 21886751 Free PMC article.
-
Schnitzler's syndrome: lessons from 281 cases.Clin Transl Allergy. 2014 Dec 5;4:41. doi: 10.1186/2045-7022-4-41. eCollection 2014. Clin Transl Allergy. 2014. PMID: 25905009 Free PMC article. Review.
-
Cryopyrin-associated periodic syndrome: an update on diagnosis and treatment response.Curr Allergy Asthma Rep. 2011 Feb;11(1):12-20. doi: 10.1007/s11882-010-0160-9. Curr Allergy Asthma Rep. 2011. PMID: 21104172 Free PMC article.
-
Does this patient have periodic fever syndrome?Clin Med (Lond). 2011 Aug;11(4):396-401. doi: 10.7861/clinmedicine.11-4-396. Clin Med (Lond). 2011. PMID: 21853843 Free PMC article. Review. No abstract available.
Publication types
MeSH terms
LinkOut - more resources
Full Text Sources
