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Case Reports
. 2008 Jul;22(7):1501-3.
doi: 10.1089/end.2007.0314.

Concurrent robotic partial adrenalectomy and extra-adrenal pheochromocytoma resection in a pediatric patient with von Hippel-Lindau disease

Craig G Rogers  1 , Adam M Blatt, George E Miles, W Marston Linehan, Peter A Pinto
Affiliations
Case Reports

Concurrent robotic partial adrenalectomy and extra-adrenal pheochromocytoma resection in a pediatric patient with von Hippel-Lindau disease

Craig G Rogers et al. J Endourol. 2008 Jul.

Abstract

Laparoscopic partial adrenalectomy is a surgical option for select patients with hereditary pheochromocytoma. We present a case of a pediatric patient with von Hippel-Lindau disease (VHL) and both an adrenal pheochromocytoma and an extra-adrenal pheochromocytoma, who underwent concurrent partial adrenalectomy and extra-adrenal pheochromocytoma resection utilizing robotic assistance. To the best of our knowledge, this is the first report of partial adrenalectomy with concurrent extra-adrenal pheochromocytoma resection.

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Figures

FIG. 1.
FIG. 1.
CT scan demonstrating a 3.0-cm left extra-adrenal mass (solid arrow) with a 0.9-cm left adrenal nodule in the apex of the left adrenal gland (dashed arrow).
FIG. 2.
FIG. 2.
Intraoperative view of robotic partial adrenalectomy. The clear view of the operative field and precision afforded by the robotic system facilitated dissection of the tumor from the normal adrenal gland.
FIG. 3.
FIG. 3.
Adrenal and extra-adrenal pheochromocytoma. (A) Representative section of adrenal tumor showing small nests of polygonal cells with amphophilic cytoplasm and round nuclei. Immunohistochemical studies performed showed positivity for chromogranin and synaptophysin, while sustentacular cells are highlighted by S-100 (data not shown) (hematoxylin and eosin, original magnification 10×). (B) Gross and histologic appearance of the extra-adrenal mass. (C) The tumor (asterisk) is surrounded by ganglion and peripheral nerve tissue (hematoxylin and eosin, original magnification 2×). The histologic features are consistent with an extra-adrenal pheochromocytoma. (D) Higher magnification view of ganglion cells (arrow) juxtaposed to the pheochromocytoma (asterisk) (hematoxylin and eosin, original magnification 10×).
See this image and copyright information in PMC

References

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