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Case Reports
. 2009 Feb;10(1):51-3.
doi: 10.1007/s10194-008-0079-x. Epub 2008 Oct 25.

CADASIL presenting as status migrainosus and persisting aura without infarction

Simona Sacco  1 , Maurizia Rasura, Marina Cao, Alessandro Bozzao, Antonio Carolei
Affiliations
Case Reports

CADASIL presenting as status migrainosus and persisting aura without infarction

Simona Sacco et al. J Headache Pain. 2009 Feb.

Abstract

Different types of migraine have been reported in 20-40% of patients with cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy (CADASIL). We describe a novel migrainous manifestation of CADASIL consisting in status migrainosus and persistent aura without infarction. The symptoms resolved after i.v. treatment with lorazepam and mannitol.

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Figures

Fig. 1
Fig. 1
Brain magnetic resonance imaging showing, on fluid-attenuated inversion recovery sequences, hyperintense lesions in the anterior part of the temporal lobes (right) and in the periventricular and subcortical regions (left)
See this image and copyright information in PMC

References

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