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Comment
. 2009 Feb 17;106(7):2093-4.
doi: 10.1073/pnas.0812934106. Epub 2009 Feb 11.

Unraveling the sterol-trafficking defect in Niemann-Pick C disease

Affiliations
Comment

Unraveling the sterol-trafficking defect in Niemann-Pick C disease

Stephen L Sturley et al. Proc Natl Acad Sci U S A. .
No abstract available

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Conflict of interest statement

The authors declare no conflict of interest.

Comment on

References

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    1. Liou HL, et al. NPC2, the protein deficient in Niemann-Pick C2 disease, consists of multiple glycoforms that bind a variety of sterols. J Biol Chem. 2006;281:36710–36723. - PubMed
    1. Infante RE, et al. NPC2 facilitates bidirectional transfer of cholesterol between NPC1 and lipid bilayers, a step in cholesterol egress from lysosomes. Proc Natl Acad Sci USA. 2008;105:15287–15292. - PMC - PubMed
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