Case Reports
doi: 10.1002/ana.410300117.
The treatable dementia of Sjögren's syndrome
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- PMID: 1929232
- DOI: 10.1002/ana.410300117
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Case Reports
The treatable dementia of Sjögren's syndrome
Ann Neurol.
1991 Jul.
Abstract
Progressive dementia developed during a 15-month period in a 56-year-old woman with serologically and clinically documented primary Sjögren's syndrome. Findings from magnetic resonance imaging and angiography were normal, but a brain biopsy disclosed perivascular lymphocytic inflammation in leptomeningeal and parenchymal vessels. Treatment with high-dose corticosteroids produced rapid and nearly complete resolution of the dementia.
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