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Case Reports
. 2009 May 18:2:7593.
doi: 10.1186/1757-1626-2-7593.

Anaesthetic management of an adult patient with DOOR syndrome: a case report

Pavel Michalek  1 , William Donaldson, Alexander Abraham
Affiliations
Case Reports

Anaesthetic management of an adult patient with DOOR syndrome: a case report

Pavel Michalek et al. Cases J. .

Abstract

We report the anaesthetic management of a 48-year-old male patient with Deafness, Onycho-Osteodystrophy and mental Retardation syndrome, epilepsy and cerebral palsy who had two dental procedures under anaesthetic care. For the first short examination sedoanalgesia was employed and the second, longer, procedure was performed under general anaesthesia. His airway management was moderately difficult and the postoperative period was complicated by partial seizures involving the upper extremity and a short period of decreased oxygen saturation. The potential anaesthetic implications of Deafness, Onycho-Osteodystrophy and mental Retardation syndrome are highlighted.

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Figures

Figure 1.
Figure 1.
Facial features of the patient with DOOR syndrome.
Figure 2.
Figure 2.
Onycho-osteodystrophy in DOOR syndrome.
See this image and copyright information in PMC

References

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