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. 1991 Jan 3;324(1):39-42.
doi: 10.1056/NEJM199101033240107.

Liver transplantation for type IV glycogen storage disease

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Liver transplantation for type IV glycogen storage disease

R Selby et al. N Engl J Med. .
No abstract available

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Figures

Figure 1
Figure 1. Myocardial Biopsy Specimens from Patient 6 (PAS-D, ×405)
Transverse sections (Panel A) and oblique sections (Panel B) of myocardial fibers in a biopsy specimen obtained 3½ weeks after liver transplantation show abundant amylopectin inclusions (red material). Panels C and D show comparable fields from a biopsy specimen obtained 14 months after transplantation, in which there is evidence of a marked decrease in the number of inclusions.

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References

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