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. 1991 Jan 3;324(1):39-42.
doi: 10.1056/NEJM199101033240107.

Liver transplantation for type IV glycogen storage disease

R Selby  1 , T E Starzl, E Yunis, B I Brown, R S Kendall, A Tzakis
Affiliations

Liver transplantation for type IV glycogen storage disease

R Selby et al. N Engl J Med. .
No abstract available

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Figures

Figure 1
Figure 1. Myocardial Biopsy Specimens from Patient 6 (PAS-D, ×405)
Transverse sections (Panel A) and oblique sections (Panel B) of myocardial fibers in a biopsy specimen obtained 3½ weeks after liver transplantation show abundant amylopectin inclusions (red material). Panels C and D show comparable fields from a biopsy specimen obtained 14 months after transplantation, in which there is evidence of a marked decrease in the number of inclusions.
See this image and copyright information in PMC

Comment in

References

    1. Anderson DH. Studies on glycogen disease with report of a case in which the glycogen was abnormal. In: Najjar VA, editor. Carbohydrate metabolism. Baltimore: Johns Hopkins Press; 1952. pp. 28–42.
    1. Illingworth B, Cori GT. Structure of glycogens and amylopectins. III. Normal and abnormal human glycogen. J Biol Chem. 1952;199:653–660. - PubMed
    1. Brown BI, Brown DH. Lack of an α-l,4-glucan:α-l,4-glucan 6-glycosyl transferase in a case of type IV glycogenosis. Proc Natl Acad Sci U S A. 1966;56:725–729. - PMC - PubMed
    1. Bannayan GA, Dean WJ, Howell RR. Type IV glycogen-storage disease: light-microscopic, electron-microscopic, and enzymatic study. Am J Clin Pathol. 1976;66:702–709. - PubMed
    1. Greene GM, Weldon DC, Ferrans VJ, et al. Juvenile polysaccharidosis with cardioskeletal myopathy. Arch Pathol Lab Med. 1987;111:977–982. - PubMed

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