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Review
. 2009 Oct;52(5):434-40.

Choledochal cysts: part 1 of 3: classification and pathogenesis

Janakie Singham  1 , Eric M Yoshida, Charles H Scudamore
Affiliations
Review

Choledochal cysts: part 1 of 3: classification and pathogenesis

Janakie Singham et al. Can J Surg. 2009 Oct.

Abstract
in English, French

Much about the etiology, pathophysiology, natural course and optimal treatment of cystic disease of the biliary tree remains under debate. Gastroenterologists, surgeons and radiologists alike still strive to optimize their roles in the management of choledochal cysts. To that end, much has been written about this disease entity, and the purpose of this 3-part review is to organize the available literature and present the various theories currently argued by the experts. In part 1, we discuss the background of the disease, describing the etiology, classification, pathogenesis and malignant potential of choledochal cysts.

Dans une large mesure, l’étiologie, la pathophysiologie, le cours naturel et le traitement optimal de la maladie kystique de l’arbre biliaire continuent de faire l’objet de débats. Les gastroentérologues, les chirurgiens et les radiologues cherchent toujours à optimiser leur rôle respectif dans la prise en charge des kystes du cholédoque. C’est pourquoi les chercheurs ont beaucoup écrit à propos de cette entité morbide, et le présent examen en 3 parties a pour objet d’organiser les études publiées et de présenter les diverses théories que font actuellement valoir les experts. Dans la première partie, nous discutons du contexte de cette maladie, en décrivant l’étiologie, la classification, la pathogenèse et le potentiel cancéreux des kystes du cholédoque.

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Figures

Fig. 1
Fig. 1
Choledochal cyst classification. (A) Type-IA cystic dilation of the extrahepatic duct. (B) Type-IB focal segmental dilation of the extrahepatic duct. (C) Type-IC fusiform dilation of the entire extrahepatic bile duct. (D) Type-II simple diverticula of the common bile duct. (E) Type-III cyst/choledochocele distal intramural dilation of the common bile duct within the duodenal wall. (F) Type-IVA combined intrahepatic and extrahepatic duct dilation. (G) Type-IVB multiple extrahepatic bile duct dilations. (H) Type-V/Caroli disease multiple intrahepatic bile duct dilation.
See this image and copyright information in PMC

References

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