Cochlear implantation in neurofibromatosis type 2 after radiation therapy

Abstract

Objective: To investigate the results of cochlear implantation in patients with neurofibromatosis Type 2 (NF2) who have previously been treated with radiation therapy to the vestibular schwannoma (VS) in their only hearing ear.

Study design: A retrospective review of the Melbourne Cochlear implant database was undertaken to identify patients with NF2 undergoing cochlear implantation in whom previous radiation therapy had been performed to control their VS (ipsilateral tumor). Three patients were identified. A case note review was undertaken and data collected on preoperative and postoperative speech perception testing.

Setting: Melbourne Cochlear implant center.

Results: All 3 patients were daily cochlear implant users. There was improvement in speech perception scores in 2 cases, with the 3rd case unable, for unrelated medical reasons, to complete postoperative testing. Subjectively, the third patient reported a dramatic improvement in communication and is a daily user of his implant.

Conclusion: Cochlear implantation results in improved hearing in a select group of NF2 patients who have undergone radiation treatment to control their VS.