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. 2008 Oct;13(4):128-31.
doi: 10.4103/0971-9261.44762.

Juvenile polyposis syndrome

Vijai D Upadhyaya  1 , A N Gangopadhyaya, S P Sharma, S C Gopal, D K Gupta, Vijayendra Kumar
Affiliations

Juvenile polyposis syndrome

Vijai D Upadhyaya et al. J Indian Assoc Pediatr Surg. 2008 Oct.

Abstract

Aim: Report of a series of 12 cases of juvenile polyposis coli.

Methods: The study period was from 1995 to 2005. All the patients were treated by total colectomy with rectal mucosectomy and endorectal ileoanal pullthrough with or without ileal pouch formation. Covering ileostomy was avoided in all the cases. Time taken for the surgery, postoperative complications and continence were documented.

Results: The mean operating time was 4.2 h (range: 4-5 h). The mean duration of hospital stay was 16.3 days (range: 15-18 days). The most common postoperative complication was pouchitis and perianal excoriation. Initially, all the patients were passing stools at an interval of 2 h, and after 3 weeks, the frequency has reduced to 6-8 stools per day. In the follow-up after 3 months, the frequency was 3-5 per day with minimal soiling.

Conclusions: Single-stage total colectomy with rectal mucosectomy and endorectal ileoanal pull-through without covering ileostomy and pouch formation is a safe and definitive treatment for juvenile polyposis coli if the patient selection is appropriate.

Keywords: Ileal pouch; juvenile polyposis syndrome; prophylactic surgery.

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Conflict of interest statement

Conflict of Interest: None declared.

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