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. 2009;54(1):59-61.
doi: 10.4103/0019-5154.48990.

Myxoid neurothekeoma: a rare soft tissue tumor of hand in a 5 month old infant

Hussah Al-Buainain  1 , Kamalesh Pal, Hossam El Shafie, Dilip K Mitra, Mohammed A Shawarby
Affiliations

Myxoid neurothekeoma: a rare soft tissue tumor of hand in a 5 month old infant

Hussah Al-Buainain et al. Indian J Dermatol. 2009.

Abstract

Myxoid Neurothekeoma is a rare benign nerve sheath tumor, commonly seen in young females. Patients usually present with a small nodule in different anatomical sites, commonly involving the face and the upper limb. We present the case of a five-month-old boy, who presented with a nodule on the left thumb. Punch biopsy and immunostaining confirmed the diagnosis of myxoid neurothekeoma. We believe this is the first reported case of myxoid neurothekeoma below 12 months of age.

Keywords: Infant; neurothekeoma; soft tissue tumor hand.

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Conflict of interest statement

Conflict of Interest: Nil.

Figures

Figure 1
Figure 1
Soft tissue nodule measuring 5 × 5 mm2 on the ventral surface of thumb
Figure 2
Figure 2
Well circumscribed lobular masses of spindle cells (arrow) in an abundant alcian blue positive mucoid (myxoid) stroma in dermis. × 100(a), × 200(b)
Figure 3
Figure 3
Hypocellular lobular mass of bland spindle cells in the dermis (H and E stain, ×100 (a), ×400 (b)
Figure 4
Figure 4
S-100 positive cells (arrow) within hypocellular lobular mass
See this image and copyright information in PMC

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