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Case Reports
. 2009:2009:976190.
doi: 10.4061/2009/976190. Epub 2009 Nov 4.

Diffuse supravalvular aortic stenosis: surgical repair in adulthood

Giovanni Ferlan  1 , Claudio De Pasquale, Concetta Losito, Annalisa Fiorella, Nicola Marraudino, Francesco Tunzi
Affiliations
Case Reports

Diffuse supravalvular aortic stenosis: surgical repair in adulthood

Giovanni Ferlan et al. Cardiol Res Pract. 2009.

Abstract

We present the case of a 54-year-old woman in which a diffuse congenital supravalvular aortic stenosis (SVAS) was associated with a severe aortic valve incompetence and heavy calcification of the aortic annulus. Repair consisted in resection of the ascending aorta, patch augmentation of the hypoplastic aortic root and annulus, placement of a 20 mm Dacron tubular graft (Vascutek, Renfrewshire, UK) and aortic valve replacement with a mechanical prosthesis (Sorin, Turin, Italy). Follow-up echocardiography demonstrated normal prosthetic valve function and a postoperative three-dimensional computed tomographic scan showed a normal shape of the reconstructed ascending aorta.

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Figures

Figure 1
Figure 1
Preoperative angiography.
Figure 2
Figure 2
Intraoperative ascending aorta specimen.
Figure 3
Figure 3
Postoperative CT angiography.
See this image and copyright information in PMC

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