Dentin dysplasia type I: a case report and review of the literature

Abstract

Introduction: Dentin dysplasia is a rare hereditary disturbance of dentin formation characterized by defective dentin development with clinically normal appearing crowns, severe hypermobility of teeth and spontaneous dental abscesses or cysts. Radiographic analysis shows obliteration of all pulp chambers, short, blunted and malformed or absent roots and peri-apical radiolucencies of non carious teeth.

Case presentation: We present a case of dentin dysplasia type I in a 12-year-old Iranian boy, and the clinical, radiographic and histopathologic findings of this condition and treatment are described.

Conclusions: There are still many inconclusive issues in the diagnosis and management of patients with dentin dysplasia. The diagnostic features of this rare disturbance will remain incompletely defined until additional cases have been described. Early diagnosis of the condition and initiation of effective regular dental treatments may help these patients to prevent or delay loss of dentition.

Figure 1

Intra-oral image before treatment.

Figure 2

View of maxillary teeth before treatment.

Figure 3

View of mandibular teeth before treatment.

Figure 4

Panoramic radiography before treatment.

Figure 5

In histopathologic examination, a variable thickness of non-keratinized stratified squamous epithelium with arch-shaped appearance is evident (×40).

Figure 6

Ground section view with stereomicroscope showing normal coronal dentin and irregular dentine obliterating the pulp chamber.